PAED-0801

PAED-0801

A 13 yr. old boy presented with difficulty in breathing on exertion. According to his mother who was also present, his exercise tolerance has been gradually worsening for the past weeks. It has reached the point where he is unable to participate in his weekly soccer match.

Cardiac catherization was performed and the results are given below.

Oxygen Saturation Levels:

• Superior vena cava: 73%
• Right atrium: 71%
• Right ventricle: 72%
• Pulmonary artery: 86%
• Left ventricle: 97%
• Aorta: 96%

Pressure Measurements:

• Right atrium: 6 mmHg
• Pulmonary artery: 53/13 mmHg
• PCWP (Pulmonary Capillary Wedge Pressure): 15 mmHg
• Left ventricle: 111/10 mmHg
• Aorta: 128/61 mmHg

Which of the following is the diagnosis?